How strict is galactose restriction in adults with galactosaemia? International practice.
نویسندگان
چکیده
Dietary management of 418 adult patients with galactosaemia (from 39 centres/12 countries) was compared. All centres advised lactose restriction, 6 restricted galactose from galactosides ± fruits and vegetables and 12 offal. 38% (n=15) relaxed diet by: 1) allowing traces of lactose in manufactured foods (n=13) or 2) giving fruits, vegetables and galactosides (n=2). Only 15% (n=6) calculated dietary galactose. 32% of patients were lost to dietetic follow-up. In adult galactosaemia, there is limited diet relaxation.
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عنوان ژورنال:
- Molecular genetics and metabolism
دوره 115 1 شماره
صفحات -
تاریخ انتشار 2015